Ebsteins anomaly of the tricuspid valve other imaging findings
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]}; Claudia P. Hochberg, M.D.; Priyamvada Singh, MBBS [3] Assistant Editor-In-Chief: Kristin Feeney, B.S. [4]
Overview
cardiac catheterization shows normal right atrial pressure most of the times, normal right ventricular (RV) pressures are present unless significant tricuspid regurgitation (TR) is present.
Indications
Given that echocardiography along with Doppler pulse imaging is quite capable of identifying patients with Ebstein’s anomaly, cardiac catheterization is not routinely performed to diagnose Ebstein’s anomaly.[1][2]
Indications for cardiac catheterization include the following:
- If closure of an atrial septal defect is considered
- For preoperative assessment of coexisting coronary heart disease
Hemodynamic Findings
- The right atrial pressure usually not increased due to the fact that the right atrium is enlarged and compliant.[1][2]
- Normal right ventricular (RV) pressures are present unless significant tricuspid regurgitation (TR) is present
- Pulmonary arterial pressures are normal or slightly decreased due to the tricuspid regurgitation and if an atrial septal defect is present, a large right-to-left shunt
- An atrial septal defect (ASD) may be present
ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease (DO NOT EDIT)[3][4]
| Class I |
| “1. Adults with Ebstein’s anomaly should have catheterization performed at centers with expertise in catheterization and management of such patients. (Level of Evidence: C)” |
References
- ↑ 1.0 1.1 Moustafa GA, Kolokythas A, Charitakis K, Avgerinos DV (2016). “Diagnostic Cardiac Catheterization in the Pediatric Population”. Curr Cardiol Rev. 12 (2): 155–62. doi:10.2174/1573403×12666160301120955. PMC 4861944. PMID 26926292.
- ↑ 2.0 2.1 Kilner PJ (December 2011). “Imaging congenital heart disease in adults”. Br J Radiol. 84 Spec No 3: S258–68. doi:10.1259/bjr/74240815. PMC 3473918. PMID 22723533.
- ↑ 3.0 3.1 Warnes CA, Williams RG, Bashore TM, Child JS, Connolly HM, Dearani JA; et al. (2008). “ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: Executive Summary: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease)”. Circulation. 118 (23): 2395–451. doi:10.1161/CIRCULATIONAHA.108.190811. PMID 18997168.
- ↑ 4.0 4.1 Warnes CA, Williams RG, Bashore TM, Child JS, Connolly HM, Dearani JA; et al. (2008). “ACC/AHA 2008 guidelines for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Develop Guidelines on the Management of Adults With Congenital Heart Disease). Developed in Collaboration With the American Society of Echocardiography, Heart Rhythm Society, International Society for Adult Congenital Heart Disease, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons”. J Am Coll Cardiol. 52 (23): e1–121. doi:10.1016/j.jacc.2008.10.001. PMID 19038677.
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