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Familial amyloidosis electrocardiogram

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Farima Kahe M.D. [2]

Overview

Findings on an ECG suggestive of familial amyloidosis include low voltage in the limb leads, AV block, atrial fibrillation and heart block.

Electrocardiogram

An ECG may be helpful in the diagnosis of familial amyloidosis. Findings on an ECG suggestive of familial amyloidosis include:[1][2]

References

  1. Dubrey SW, Cha K, Skinner M, LaValley M, Falk RH (July 1997). “Familial and primary (AL) cardiac amyloidosis: echocardiographically similar diseases with distinctly different clinical outcomes”. Heart. 78 (1): 74–82. doi:10.1136/hrt.78.1.74. PMC 484868. PMID 9290406.
  2. Falk RH (September 2005). “Diagnosis and management of the cardiac amyloidoses”. Circulation. 112 (13): 2047–60. doi:10.1161/CIRCULATIONAHA.104.489187. PMID 16186440.

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