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Hamman-Rich syndrome epidemiology and demographics

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Chandrakala Yannam, MD [2]

Overview

The world wide incidence of acute interstitial pneumonitis is approximately 97 cases per 100,000 individuals. The prevalence of acute interstitial pneumonitis is not known. Acute interstitial pneumonitis affects men and women equally. Acute interstitial pneumonitis occur typically previously healthy individuals in the age group of 50 to 55years.

Epidemiology and Demographics

Incidence

Prevalence

Case-fatality rate/Mortality rate

  • Case fatality rate is high approximately 27%-78%.[1][3]
  • The mean time from symptom onset to death was approximately 20 days – 6 months.

Age

Race

Gender

Region

References

  1. 1.0 1.1 1.2 Vourlekis JS, Brown KK, Cool CD, Young DA, Cherniack RM, King TE, Schwarz MI (November 2000). “Acute interstitial pneumonitis. Case series and review of the literature”. Medicine (Baltimore). 79 (6): 369–78. PMID 11144035.
  2. Olson J, Colby TV, Elliott CG (December 1990). “Hamman-Rich syndrome revisited”. Mayo Clin. Proc. 65 (12): 1538–48. PMID 2255216.
  3. Quefatieh A, Stone CH, DiGiovine B, Toews GB, Hyzy RC (August 2003). “Low hospital mortality in patients with acute interstitial pneumonia”. Chest. 124 (2): 554–9. PMID 12907542.

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