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Kasabach-Merritt syndrome overview

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Kasabach-Merritt Syndrome (KMS) is a rare disease, usually of infants, in which a vascular tumor leads to decreased platelet counts and sometimes other bleeding problems,[1] which can be life-threatening.[2] It is also known as hemangioma thrombocytopenia syndrome.

References

  1. Hall G (2001). “Kasabach-Merritt syndrome: pathogenesis and management”. Br J Haematol. 112 (4): 851–62. PMID 11298580.
  2. Shim W (1968). “Hemangiomas of infancy complicated by thrombocytopenia”. Am J Surg. 116 (6): 896–906. PMID 4881491.

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