Primary ciliary dyskinesia electrocardiogram

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Hafsa Ghaffar, M.B.B.S[2]

Primary ciliary dyskinesia occasionally presents with dextrocardia and situs inversus totalis, non functioning cilia in the embryonal node could be responsible for this mal positioning. Ecg shows right axis deviation, a finding if present should warrant further testing.

Primary ciliary dyskinesia is occasionally associated with situs inversus totalis and dextrocardia. Ecg could detect dextrocardia and warrant for additional testing in individuals. Ecg demonstrates the following changes:

• Prominent right axis deviation.
• Positive QRS complexes with upright P and T waves in aVR leads.
• Inversion of all complexes, also known as ‘global negativity’ with inverted P wave, negative QRS, inverted T wave in Lead 1.
• Absent R-wave progression in the precordial leads and dominant S waves throughout.^[1]

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