Shone's syndrome

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Shone’s syndrome consists of a set of four cardiac defects: a supravalve mitral membrane (SVMM), parachute mitral valve, subaortic stenosis (membranous or muscular) and coarctation of the aorta. Essentially, it is both a left ventricular inflow and outflow obstruction. The prognosis is inversely related to the degree of obstruction caused by the SVMM.^[1] The SVMM is also first to develop and likely causes the development of the other three defects.

References

↑ Zucker, N.; Levitas, A.; Zalzstein, E. (2004). “Prenatal diagnosis of Shone’s syndrome: parental counseling and clinical outcome”. Ultrasound Obstet Gynecol. 24 (6): 629–32. doi:10.1002/uog.1753. PMID 15517547. Unknown parameter |month= ignored (help)

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[Zucker-2004-1] Zucker, N.; Levitas, A.; Zalzstein, E. (2004). “Prenatal diagnosis of Shone’s syndrome: parental counseling and clinical outcome”. Ultrasound Obstet Gynecol. 24 (6): 629–32. doi:10.1002/uog.1753. PMID 15517547. Unknown parameter |month= ignored (help)

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