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The heart in Behçet's disease

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Approximately 5% of patients with Behcet’s disease have associated cardiovascular disease.

Cardiovascular Conditions Associated with Behcet’s Disease

The following cardiac abnormalities have been associated with Behcet’s disease:

  1. Aortic insufficiency due to a proximal aortitis
  2. Intra cardiac thrombosis
  3. Myocardial infarction[1]
  4. Pericarditis
  5. Endocarditis
  6. Mitral Valve Prolapse
  7. Endomyocardial fibrosis
  8. Arrhythmias
  9. Coronary artery vasculitis[2]
  10. Myocarditis

Vascular manifestations

  1. Superficial thrombophlebitis
  2. Deep venous thrombophlebitis
  3. Small vessel vasculitis
  4. Arterial Occlusion and/or Aneurysms

Sources

Al-Otaibi LM, Porter SR, Poate TW (2005). “Behçet’s disease: a review”. J. Dent. Res. 84 (3): 209–22. PMID 15723859. Unknown parameter |month= ignored (help)

References

  1. Schirmer M, Weidinger F, Sandhofer A, Gschwendtner A, Wiedermann C. Valvular disease and myocardial infarctions in a patient with Behçet disease. J Clin Rheumatol. Oct 2003;9(5):316-20.
  2. Schirmer M, Weidinger F, Sandhofer A, Gschwendtner A, Wiedermann C. Valvular disease and myocardial infarctions in a patient with Behçet disease. J Clin Rheumatol. Oct 2003;9(5):316-20.

http://www.behcet.org.il/symptoms&outcomesE.htm


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