Health Dictionary
Reliable, easy-to-read patient information on common medical conditions — written in plain language, free of jargon, and grounded in current evidence. Browse the most frequent diagnoses, understand what they mean for everyday life, and learn which steps and questions help you have a focused conversation with your doctor.
Arnold-Chiari malformation epidemiology and demographics
Introduction
Overview
Overview
The prevalence of Arnold Chiari malformation is unknown since most of the cases are accidentally found. The mortality rate of Arnold Chiari malformation depends on the subtype but type 3 has the highest mortality rate as a result of respiratory failure in infancy. Arnold Chiari malformation commonly affects adolescence and adulthood, but also has been seen in younger children. There is no racial predilection to Arnold Chiari malformation.
Epidemiology and Demographics
Epidemiology and Demographics
Prevalence
- The prevalence of Arnold Chiari malformation is unknown since most of the cases are accidentally found.[1]
- It is believed that approximate prevalence is 0.1 to 0.5 percent worldwide.
Mortality rate
- The mortality rate of Arnold Chiari malformation depends on the subtype.
- Type 3 has the highest mortality rate as a result of respiratory failure in infancy.
Age
- Arnold Chiari malformation commonly affects adolescence and adulthood, but also has been seen in younger children.
Race
- There is no racial predilection to Arnold Chiari malformation.
- Arnold Chiari malformation usually presents with back pain in whites and lower extremity weakness in African-Americans.
Gender
- Women are more commonly affected by Arnold Chiari malformation than men. The women to men ratio is approximately 3 to 1.
References
References
- ↑ Schijman E (May 2004). “History, anatomic forms, and pathogenesis of Chiari I malformations”. Childs Nerv Syst. 20 (5): 323–8. doi:10.1007/s00381-003-0878-y. PMID 14762679.
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Fahimeh Shojaei, M.D.