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Reliable, easy-to-read patient information on common medical conditions — written in plain language, free of jargon, and grounded in current evidence. Browse the most frequent diagnoses, understand what they mean for everyday life, and learn which steps and questions help you have a focused conversation with your doctor.

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Atypical teratoid rhabdoid tumor epidemiology and demographics

Introduction

Overview

Overview

Atypical teratoid rhabdoid tumor comprises approximately 1 – 2% of all pediatric brain tumors; however, in patients less than 3 years of age, this tumor accounts for up to 20% of cases. The incidence of atypical teratoid rhabdoid tumor is approximately 0.3 per 100,000 individuals in the United States. Atypical teratoid rhabdoid tumor is a rare disease that tends to affect the children. The median age at diagnosis is approximately 24 – 30 months. Males are more commonly affected with atypical teratoid rhabdoid tumor than females. The male to female ratio is approximately 1.9 to 1.

Epidemiology and Demographics

Epidemiology and Demographics

Incidence

  • The incidence of atypical teratoid rhabdoid tumor is approximately 0.3 per 100,000 individuals in the United States.[1]

Prevalence

  • Atypical teratoid rhabdoid tumor comprises approximately 1 – 2% of all pediatric brain tumors; however, in patients less than 3 years of age, this tumor accounts for up to 20% of cases.[2]

Age

  • Atypical teratoid rhabdoid tumor is a rare disease that tends to affect the children.[3][4]
  • However, although rare, atypical teratoid rhabdoid tumor has also been reported in adult patients.[5]
  • The median age at diagnosis is approximately 24 – 30 months.[6]

Race

  • There is no racial predilection to atypical teratoid rhabdoid tumor.

Gender

  • Males are more commonly affected with atypical teratoid rhabdoid tumor than females. The male to female ratio is approximately 1.9 to 1.[2]
References

References

  1. ↑ Atypical teratoid rhabdoid tumor. Wikipedia 2015. https://en.wikipedia.org/wiki/Atypical_teratoid_rhabdoid_tumor. Accessed on December 10, 2015
  2. ↑ 2.0 2.1 Ginn, Kevin F.; Gajjar, Amar (2012). “Atypical Teratoid Rhabdoid Tumor: Current Therapy and Future Directions”. Frontiers in Oncology. 2. doi:10.3389/fonc.2012.00114. ISSN 2234-943X.
  3. ↑ Epidemiology of atypical teratoid rhabdoid tumor. Dr Bruno Di Muzio and Frank Gaillard et al. Radiopaedia 2015. http://radiopaedia.org/articles/atypical-teratoidrhabdoid-tumour. Accessed on December 10, 2015
  4. ↑ Clinical presentation of atypical teratoid rhabdoid tumor. National Cancer Institute 2015. http://www.cancer.gov/types/brain/hp/child-cns-atrt-treatment-pdq#link/_113_toc. Accessed on December 16, 2015
  5. ↑ Udaka, Y. T.; Shayan, K.; Chuang, N. A.; Crawford, J. R. (2013). “Atypical Presentation of Atypical Teratoid Rhabdoid Tumor in a Child”. Case Reports in Oncological Medicine. 2013: 1–4. doi:10.1155/2013/815923. ISSN 2090-6706.
  6. ↑ Slavc, Irene; Chocholous, Monika; Leiss, Ulrike; Haberler, Christine; Peyrl, Andreas; Azizi, Amedeo A.; Dieckmann, Karin; Woehrer, Adelheid; Peters, Christina; Widhalm, Georg; Dorfer, Christian; Czech, Thomas (2014). “Atypical teratoid rhabdoid tumor: improved long-term survival with an intensive multimodal therapy and delayed radiotherapy. The Medical University of Vienna Experience 1992-2012”. Cancer Medicine. 3 (1): 91–100. doi:10.1002/cam4.161. ISSN 2045-7634.

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Associate Editor(s)-in-Chief: Sujit Routray, M.D. [2]