Autoimmune lymphoproliferative syndrome surgery

No definitive surgery is required to treat Autoimmune lymphoproliferative syndrome(ALPS).

Splenectomy is the only surgery used to treat ALPS. But splenectomy is reserved as the last treatment option in patients with severe refractory cytopenias, severe hypersplenism to avoid the high risk of recurrence cytopenias and sepsis in post-splenectomy patients with ALPS.^[1]