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Caroli's disease epidemiology and demographics

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Epidemiology and Demographics

Epidemiology and Demographics

  • The disease is uncommon, with about 180 cases reported in the literature.
  • The disease affects about 1 in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease.
  • Biliary cysts are more common in Japan and in young women.
  • Females are more prone to Caroli disease than males.
References

References

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