11β-hydroxylase deficiency surgery

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Mehrian Jafarizade, M.D [2]

Overview

In patients with 11β-hydroxylase deficiency, girls with ambiguous genitalia mostly undergo reconstructive surgery such as clitoroplasty and vaginoplasty.

Surgery

In patients with 11β-hydroxylase deficiency, girls with ambiguous genitalia mostly undergo reconstructive surgery such as clitoroplasty and vaginoplasty. In clitoral reduction surgery neurovascular bundle, the glans, and the preputial skin related to the glans should be kept completely.^[1]^[2]

References

↑ Premawardhana LD, Hughes IA, Read GF, Scanlon MF (1997). “Longer term outcome in females with congenital adrenal hyperplasia (CAH): the Cardiff experience”. Clin Endocrinol (Oxf). 46 (3): 327–32. PMID 9156043.
↑ Hendren WH, Donahoe PK (1980). “Correction of congenital abnormalities of the vagina and perineum”. J. Pediatr. Surg. 15 (6): 751–63. PMID 7007606.

Overview