Idiopathic pulmonary fibrosis is a disease among a large group of the interstitial lung diseases and particularly a subtype of the idiopathic interstitial pneumonia. The major group include acute interstitial pneumonia (AIP), cryptogenic organizing pneumonia (COP), respiratory bronchiolitis–interstitial lung disease (RB-ILD), and desquamative interstitial pneumonia (DIP).

• Idiopathic pulmonary fibrosis is a disease among a large group of the interstitial lung diseases and particularly a subtype of the idipathic interstitial pneumonia. The major forms of the idiopathic interstitial pneumonia include:
• The idiopathic interstitial pneumonias are classified by the American Thoracic Society/European Respiratory Society (ATS/ERS) into three main groups:^[1]
  • Major idiopathic interstitial pneumonia
  • Rare idiopathic interstitial pneumonia
  • Unclassifiable idiopathic interstitial pneumonia
• The idiopathic interstitial fibrosis is the chronic form of the idiopathic interstitial pneumonia. Other forms of the idiopathic interstitial pneumonia include the following:
  • Acute or subacute: Acute interstitial pneumonia (AIP) and cryptogenic organizing pneumonia (COP)
  • Chronic: Idiopathic pulmonary fibrosis (IPF)
  • Smoking-related: Respiratory bronchiolitis–interstitial lung disease (RB-ILD) and desquamative interstitial pneumonia (DIP)

[[Category:Primary Care]