Idiopathic pulmonary fibrosis classification
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ahmed Elsaiey, MBBCH [2]
Overview
Overview
Idiopathic pulmonary fibrosis is a disease among a large group of the interstitial lung diseases and particularly a subtype of the idiopathic interstitial pneumonia. The major group include acute interstitial pneumonia (AIP), cryptogenic organizing pneumonia (COP), respiratory bronchiolitis–interstitial lung disease (RB-ILD), and desquamative interstitial pneumonia (DIP).
Classification
Classification
- Idiopathic pulmonary fibrosis is a disease among a large group of the interstitial lung diseases and particularly a subtype of the idipathic interstitial pneumonia. The major forms of the idiopathic interstitial pneumonia include:
- The idiopathic interstitial pneumonias are classified by the American Thoracic Society/European Respiratory Society (ATS/ERS) into three main groups:[1]
- Major idiopathic interstitial pneumonia
- Rare idiopathic interstitial pneumonia
- Unclassifiable idiopathic interstitial pneumonia
- The idiopathic interstitial fibrosis is the chronic form of the idiopathic interstitial pneumonia. Other forms of the idiopathic interstitial pneumonia include the following:
- Acute or subacute: Acute interstitial pneumonia (AIP) and cryptogenic organizing pneumonia (COP)
- Chronic: Idiopathic pulmonary fibrosis (IPF)
- Smoking-related: Respiratory bronchiolitis–interstitial lung disease (RB-ILD) and desquamative interstitial pneumonia (DIP)
References
References
- ↑ “American Thoracic Society/European Respiratory Society International Multidisciplinary Consensus Classification of the Idiopathic Interstitial Pneumonias”. American Journal of Respiratory and Critical Care Medicine. 165 (2): 277–304. 2002. Unknown parameter
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