Lymphangiomyomatosis (patient information)

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ammu Susheela, M.D. [2]

Overview

Symptoms of lymphangiomyomatosis may include constipation, dyspnea, and cough. Lymphangiomyomatosis may be diagnosed using CT,Xray, and immunohistochemistry. The mainstay of therapy for lymphangiomyomatosisis include sirolimus, medroxyprogesterone, gonadotropin-releasing hormone agonists, and tamoxifen. Common complications of lymphangiomyomatosis include ascitis, chylous pleural effusion, pneumothorax, hemoptysis, chyloptysis, chyluria, hematuria, pericardial effusion, pneumoperitoneum, lymphedema, respiratory failure, osteoporosis, and meningioma.

What are the symptoms of Lymphangiomatosis?

Symptoms of lymphangiomyomatosis may include constipation, difficulty breathing, and cough.

Diagnosis

Lymphangiomyomatosis may be diagnosed using CT,Xray, and immunohistochemistry.

Treatment options

The mainstay of therapy for lymphangiomyomatosisis include sirolimus, medroxyprogesterone, gonadotropin-releasing hormone agonists, and tamoxifen.

Possible complications

Common complications of lymphangiomyomatosis include ascitis, chylous pleural effusion, pneumothorax, hemoptysis, chyloptysis, chyluria, hematuria, pericardial effusion, pneumoperitoneum, lymphedema, respiratory failure, osteoporosis, and meningioma.

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