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Health Dictionary

Reliable, easy-to-read patient information on common medical conditions — written in plain language, free of jargon, and grounded in current evidence. Browse the most frequent diagnoses, understand what they mean for everyday life, and learn which steps and questions help you have a focused conversation with your doctor.

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Malignant peripheral nerve sheath tumor epidemiology and demographics

Introduction

Overview

Overview

Malignant peripheral nerve sheath tumors comprise ∼2% of all sarcomas whichare a small fraction of a group of cancers that affect 5 people per million per year. The incidence of malignant peripheral nerve sheath tumor is approximately 0.1 per 100,000 individuals worldwide.[1] The incidence of malignant peripheral nerve sheath tumor increases with age.[1] Malignant peripheral nerve sheath tumor affects men and women equally.[2]

Incidence

Incidence

  • Malignant peripheral nerve sheath tumors comprise ∼2% of all sarcomas whichare a small fraction of a group of cancers that affect 5 people per million per year.
  • The incidence of malignant peripheral nerve sheath tumor is approximately 0.1 per 100,000 individuals worldwide.[1]
  • Malignant peripheral nerve sheath tumor may arise at any age with no gender predilection.
  • Half of MPNSTs are associated with neurofibromatosis type 1 (NF1), the autosomal dominant condition that, affecting 1 in 3000 live births, represents the most common human cancer genetic predisposition syndrome.
Age

Age

  • Malignant peripheral nerve sheath tumor may arise at any age with no gender predilection and affects men and women equally .[1]
Gender

Gender

  • Malignant peripheral nerve sheath tumor may arise at any age with no gender predilection and affects men and women equally.[2]
References

References

  1. ↑ 1.0 1.1 1.2 1.3 Bates JE, Peterson CR, Dhakal S, Giampoli EJ, Constine LS (2014). “Malignant peripheral nerve sheath tumors (MPNST): a SEER analysis of incidence across the age spectrum and therapeutic interventions in the pediatric population”. Pediatr Blood Cancer. 61 (11): 1955–60. doi:10.1002/pbc.25149. PMID 25130403.
  2. ↑ 2.0 2.1 Malignant peripheral nerve sheath tumor. Radiopaedia 2015. http://radiopaedia.org/articles/malignant-peripheral-nerve-sheath-tumour

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Marjan Khan M.B.B.S.[2]