Health Dictionary
Reliable, easy-to-read patient information on common medical conditions — written in plain language, free of jargon, and grounded in current evidence. Browse the most frequent diagnoses, understand what they mean for everyday life, and learn which steps and questions help you have a focused conversation with your doctor.
Mondini dysplasia
Introduction
Mondini Dysplasia, (also known as Mondini malformation and Mondini defect) is an abnormality in the inner ear that can be the cause of hearing loss.
A person with Mondini dysplasia has a cochlea that is incomplete. A normal cochlea has two and a half turns, a cochlea with Mondina dysplasia has two, one and a half, one, or no turns (or increments, obviously). This results in gradual or even sudden hearing loss that may be profound.“case history”.