Noncompaction cardiomyopathy electrocardiogram
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Overview
There may be evidence of[1][2][3][4][5]:
- Wolf-Parkinson-White syndrome (in 15% of children[6][7], not in adults[8])
- Bundle branch block (mostly in adults)
- Heart block (mostly in adults)
- Biventricular hypertrophy
- Large QRS voltages
- Diffuse T wave inversions
- Arrhythmias
Presentation in Children
Presentation in Children
Children may present with Wolf-Parkinson-White syndrome (WPW) which may require ablation and or defibrillator implantation.
Presentation in Adults
Presentation in Adults
In adults, the most common form of presentation is a bundle branch block or atrioventricular block.
References
References
- ↑ Ritter M, Oechslin E, Sutsch G, et al. Isolated noncompaction of the myocardium in adults. Mayo Clin Proc. 1997; 72: 26–31.
- ↑ Chin TK, Perloff JK, Williams RG, et al. Isolated noncompaction of left ventricular myocardium: a study of eight cases. Circulation. 1990; 82: 507–513.
- ↑ Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.
- ↑ Ichida F, Hanamichi Y, Miyawaki T, et al. Clinical features of isolated noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background. J Am Coll Cardiol. 1999; 34: 233–240.
- ↑ Reynen K, Bachmann K, Singer H. Spongy myocardium. Cardiology. 1997; 88: 601–602.
- ↑ Ichida F, Hanamichi Y, Miyawaki T, et al. Clinical features of isolated noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background. J Am Coll Cardiol. 1999; 34: 233–240.
- ↑ Yasukawa K, Terai M, Honda A, et al. Isolated noncompaction of ventricular myocardium associated with fatal ventricular fibrillation. Pediatr Cardiol. 2001; 22: 512–514.
- ↑ Ritter M, Oechslin E, Sutsch G, et al. Isolated noncompaction of the myocardium in adults. Mayo Clin Proc. 1997; 72: 26–31.
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