Health Dictionary
Reliable, easy-to-read patient information on common medical conditions — written in plain language, free of jargon, and grounded in current evidence. Browse the most frequent diagnoses, understand what they mean for everyday life, and learn which steps and questions help you have a focused conversation with your doctor.
Porphyria natural history
Introduction
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Overview
Overview
Natural History
Natural History
Complications
Complications
- Patients with hepatic porphyrias (PCT, AIP, HCP, VP) are at increased risk over their life for hepatocellular carcinoma (primary liver cancer) and may require monitoring. Other typical risk factors for liver cancer need not be present, such as hepatitis B or C, iron overload or alcoholic cirrhosis.
- The neuropathic effects can progress and become severe leading to irreversible neurologic damage
- Guillian-Barre type syndrome with paralysis
- Bulbar dysfunction
- Respiratory failure
- Death
Prognosis
Prognosis
References
References
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: