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Noncompaction cardiomyopathy

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editors-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]

Synonyms and keywords: left ventricular noncompaction, LVNC, NCC, spongiform cardiomyopathy, (Isolated) noncompaction of the ventricular myocardium, (I)NVM, non-compaction of the left ventricular myocardium, left ventricular hypertrabeculation, spongy myocardium.

Pathophysiology

Embryology | Histology | Genetics | Left ventricular dysfunction | Thromboembolism | Neuromuscular disorders

Diagnosis

History & Symptoms | Physical Examination | Laboratory Studies | Genetic Testing | Electrocardiogram | Chest X Ray | Echocardiography | MRI | CT | Biopsy

Management

Medical Therapy | Surgery

See also

Cardiomyopathy, Barth syndrome, Emery-Dreifuss muscular dystrophy, myotubular myopathy, genes responsible for NCC are located also in the area that cause these conditions.


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